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Management of Kawasaki Disease and its Cardiac Sequelae

متطلبات الإكمال
"last update: 3 December  2025"                                                                                      Download Guideline

- Abbreviations

ACEI

Angiotensin Converting Enzyme inhibitors

ACR/VF

American College of Rheumatology/Vasculitis Foundation

Adolopment

Adoption-Adaptation-Development

AGREE II

Appraisal of Guidelines for Research and Evaluation Instrument

Anti-TNF α

Anti-tumor necrosis factor alpha

ARB

Angiotensin Receptor Blocker

ASA

Acetyl salicylic acid

AST

Aspartate aminotransferase

ALT

Alanine Transaminase

ANA

Antinuclear Antibodies

ANCA

Antineutrophil cytoplasm antibodies

BB

Beta Blocker

BCG

Bacille Calmette Guerin

C3

Complement 3

CAA

Coronary artery aneurysm

CABG

Coronary artery bypass graft

CAL

Coronary artery lesion

CDC

Center of Disease Control

CHF

Congestive Heart Failure

CKD

Complete Kawasaki Disease

CNS

Central Nervous System

COVID 19

Coronavirus disease 2019

CPG

Clinical Practice Guideline

CRP

C- reactive protein

CTA

Computed Tomographic angiography

DHS

Demographic and Health Survey

DMARDs

Disease Modifying Anti-Rheumatic Drugs

DOACs

Direct oral anticoagulants

EBV

Epstein Bar virus

EPG

Egyptian Pediatrics Clinical Practice Guidelines Committee

EPG CPG

EPG Clinical Practice Guideline

ERG

External Review Group

ESR

Erythrocyte Sedimentation Rate

GAG

Guideline Adaptation Group

GDG

Guideline Development Group

GPS

Good Practice Statement

GU

Genitourinary

GRADE

Grading of Recommendations Assessment, Development and Evaluation

GI

Gastrointestinal

Hs

High sensitivity

HPF

High power field

IKD

Incomplete Kawasaki Disease

IVIG

Intravenous immunoglobulins

JCS

Japanese circulation society

JSCS

Japanese Society of Cardiovascular surgery

KD

Kawasaki Disease

KDSS

Kawasaki disease Shock Syndrome

LDA

Low dose Aspirin

LVEF

Left ventricular Ejection Fraction

LVSF

Left Ventricular Shortening Fraction

MAS

Macrophage activation syndrome

MIS-C

Multisystem inflammatory syndrome in children

MP

Methylprednisolone

MRI

Magnetic resonance imaging

NHS

The National Health Service

NSTE-ACS

non–ST-segment–elevation acute coronary syndrome;

NT-proBNP

N-terminal prohormones of brain natriuretic peptide

PAN

Polyarteritis Nodosa

PCI

Percutaneous coronary intervention

PCR

Polymerase chain reaction

PICO

Population, intervention, comparison, and outcomes

PIPOH

 

Patient population, intervention, Professional, outcomes, and healthcare context

RIGHT

A Reporting Tool for Practice Guidelines in Health Care

SARS COV2

Severe Acute Respiratory syndrome corona virus 2

SHARE

Single Hub and Access point for pediatric Rheumatology in Europe

SIP

Societa Italiana Di Pediatria (Italian Society of Pediatrics)

STEMI

ST-segment–elevation myocardial infarction

TEE

Transesophageal echocardiography

TNF

Tumor necrosis factor

tPA

Tissue-type plasminogen activator

WBC

White Blood Cell Count